Inborn errors of metabolism:
Indications for CARNITOR ORAL SOLUTION:
Primary systemic or secondary carnitine deficiency.
Consume slowly in divided doses, preferably with meals; may mix in liquids. Initially 1g/day; titrate slowly; range 1–3g/day.
Consume slowly in divided doses, preferably with meals; may mix in liquids. Initially 50mg/kg/day; titrate slowly; range 50–100mg/kg (max 3g) per day.
Obtain baseline carnitine level; monitor blood chemistry, carnitine levels, vital signs, clinical condition. Seizure disorders. Renal insufficiency (oral forms). Pregnancy. Nursing mothers: not recommended.
Monitor INR with warfarin.
GI upset/pain, body odor, seizures; hypersensitivity reactions (discontinue if occur). Inj: also inj site reactions.
Tabs—90; Oral soln—118mL; Single-dose vials (5mL)—5